Item 1 of 1 (back to results) sapropterin dihydrochloride The dihydrochloride salt of sapropterin. It is used for the diagnosis and treatment of variant forms of phenylketonuria (hyperphenylalaninaemia) associated with tetrahydrobiopterin deficiency. Natural cofactor for phenylalanine hydroxylase, tyrosine hydroxylase, tryptophan hydroxylase, and nitric oxide synthetase.

Current search: 03. Biological Effects of Specific Chemicals: biochemical uses [CHEBI:52206] > cofactor [CHEBI:23357] > coenzyme [CHEBI:23354] > sapropterin dihydrochloride [CHEBI:32120] × Select any link to see items in a related category. more general categories    information about this item 03. Biological Effects of Specific Chemicals  03. Biological Effects of Specific Chemicals  biochemical uses [CHEBI:52206] (3306)   cofactor [CHEBI:23357] (40)   coenzyme [CHEBI:23354] (24)   sapropterin dihydrochloride [CHEBI:32120] (1) 05. Industrial Uses  05. Industrial Uses  pharmaceutical [CHEBI:52217] (1978)   diagnostic agent [CHEBI:33295] (53)   sapropterin dihydrochloride [CHEBI:32120] (1) 08. Chemical Category  08. Chemical Category  main group molecular entity [CHEBI:33579] (25650)   p-block molecular entity [CHEBI:33675] (25343)   halogen molecular entity [CHEBI:24471] (1475)   chlorine molecular entity [CHEBI:23117] (884)   chloride salt [CHEBI:23114] (326)   organic chloride salt [CHEBI:36094] (294)   hydrochloride [CHEBI:36807] (240)   sapropterin dihydrochloride [CHEBI:32120] (1)  halide [CHEBI:37578] (1402)   halide salt [CHEBI:33958] (423)   chloride salt [CHEBI:23114] (326)   organic chloride salt [CHEBI:36094] (294)   hydrochloride [CHEBI:36807] (240)   sapropterin dihydrochloride [CHEBI:32120] (1)  polyatomic entity [CHEBI:36357] (18777)   heteroatomic molecular entity [CHEBI:37577] (13672)   salt [CHEBI:24866] (931)   organic salt [CHEBI:24868] (775)   organic halide salt [CHEBI:51069] (386)   organic chloride salt [CHEBI:36094] (294)   hydrochloride [CHEBI:36807] (240)   sapropterin dihydrochloride [CHEBI:32120] (1)  halide salt [CHEBI:33958] (423)   chloride salt [CHEBI:23114] (326)   organic chloride salt [CHEBI:36094] (294)   hydrochloride [CHEBI:36807] (240)   sapropterin dihydrochloride [CHEBI:32120] (1)  halide [CHEBI:37578] (1402)   halide salt [CHEBI:33958] (423)   chloride salt [CHEBI:23114] (326)   organic chloride salt [CHEBI:36094] (294)   hydrochloride [CHEBI:36807] (240)   sapropterin dihydrochloride [CHEBI:32120] (1) ChEBI Compound Accession Identifier:   [CHEBI:32120] ChEBI Compound Description:   The dihydrochloride salt of sapropterin. It is used for the diagnosis and treatment of variant forms of phenylketonuria (hyperphenylalaninaemia) associated with tetrahydrobiopterin deficiency. Natural cofactor for phenylalanine hydroxylase, tyrosine hydroxylase, tryptophan hydroxylase, and nitric oxide synthetase. ChEBI Compound Identification Number:   32120 ChEBI InChI Value:   "InChI=1S/C9H15N5O3.2ClH/c1-3(15)6(16)4-2-11-7-5(12-4)8(17)14-9(10)13-7;;/h3-4,6,12,15-16H,2H2,1H3,(H4,10,11,13,14,17);2*1H/t3-,4+,6-;;/m0../s1" ChEBI InChIKey Value:   RKSUYBCOVNCALL-NTVURLEBSA-N ChEBI Compound Name:   sapropterin dihydrochloride ChEBI SMILES Value:   Cl.Cl.[H][C@@]1(CNc2nc(N)[nH]c(=O)c2N1)[C@@H](O)[C@H](C)O ChEBI Substance ID:   93581336 ChEBI URL:   ChEBI:32120 ChemSpider ID:   NS Ontomatica Chemical Accession Key (OnChAKey):   RKSUYBCOVNCALL_NTVURLEBSA_N_000_000000 PubChem Compound ID:   636369